Publikationen Zentrum für seltene Hormonstörungen

2022

Beun JG, Burman P, Kämpe O, Husebye ES, Hahner S, Kristensen J, Noordzij A, Dahlqvist P (2022)
Doctors, teach your adrenal insufficiency patients well: provide them with a European Emergency Card!
Endocrine Connections 2022 Dec 12; 12(1): e220345

Zur Publikation 

Chifu I, Hahner S (2022)
Nebennieren-Erkrankungen: Morbus Addison [Adrenal gland diseases: Addison's Disease].
Deutsche Medizinische Wochenschrift 2022 Jan; 147(3): 98-106

Zur Publikation

Chifu I, Weng AM, Burger-Stritt S, Bley TA, Christa M, Köstler H, Hahner S (2022)
Non-invasive assessment of tissue sodium content in patients with primary adrenal insufficiency.
European Journal of Endocrinology 2022 Jul 21; 187(3): 383-390 

Zur Publikation

Christa M, Hahner S, Köstler H, Bauer WR, Störk S, Weng AM (2022)
Primary hyperaldosteronism induces congruent alterations of sodium homeostasis in different skeletal muscles: a 23Na-MRI study.
European Journal of Endocrinology 2022 Mar 29; 186(5): K33-K38

Zur Publikation

Deutschbein T, Reimondo G, Di Dalmazi G, Bancos I, Patrova J, Vassiliadi DA, Nekić AB, Debono M, Lardo P, Ceccato F, Petramala L, Prete A, Chiodini I, Ivović M, Pazaitou-Panayiotou K, Alexandraki KI, Hanzu FA, Loli P, Yener S, Langton K, Spyroglou A, Kocjan T, Zacharieva S, Valdés N, Ambroziak U, Suzuki M, Detomas M, Puglisi S, Tucci L, Delivanis DA, Margaritopoulos D, Dusek T, Maggio R, Scaroni C, Concistrè A, Ronchi CL, Altieri B, Mosconi C, Diamantopoulos A, Iñiguez-Ariza NM, Vicennati V, Pia A, Kroiss M, Kaltsas G, Chrisoulidou A, Marina LV, Morelli V, Arlt W, Letizia C, Boscaro M, Stigliano A, Kastelan D, Tsagarakis S, Athimulam S, Pagotto U, Maeder U, Falhammar H, Newell-Price J, Terzolo M, Fassnacht M (2022)
Age-dependent and sex-dependent disparity in mortality in patients with adrenal incidentalomas and autonomous cortisol secretion: an international, retrospective, cohort study.
The Lancet: Diabetes & Endocrinology 2022 Jul; 10(7): 499-508.

Zur Publikation

Fuss CT, Brohm K, Fassnacht M, Kroiss M, Hahner S (2022)
Reassessment of Postural Stimulation Testing as a Simple Tool to Identify a Subgroup of Patients With Unilateral Primary Aldosteronism.
The Journal of Clinical Endocrinology & Metabolism 2022 Jan 18; 107(2): e865-e873.

Zur Publikation

Herbert SL, Ergezinger K, Sauer S, Kurz F, Schlaiß T, Wöckel A, Albert US (2022)
Prepubertal Idiopathic Unilateral Gynecomastia: Case Report and Literature Review.
Breast Care (Basel) 2022 Dec; 17(6): 573-579

Zur Publikation 

Nagel K, Hendricks A, Lenschow C, Meir M, Hahner S, Fassnacht M, Wiegering A, Germer CT, Schlegel N (2022)
Definition and diagnosis of postsurgical hypoparathyroidism after thyroid surgery: meta-analysis.
BJS Open 2022 Sep 2; 6(5): zrac102

Zur Publikation

2020

Adolf C, Braun LT, Fuss CT, Hahner S, Kunzel H, Handgriff L, Sturm L, Heinrich DA, Schneider H, Bidlingmaier M, Reincke M (2020)
Spironolactone reduces biochemical markers of bone turnover in postmenopausal women with primary aldosteronism.
Endocrine 2020 Jun 27; 69: 625-633
Zur Publikation 

Bothou C, Anand G, Li D, Kienitz T, Seejore K, Simeoli C, Ebbehoj A, Ward EG, Paragliola RM, Ferrigno R, Badenhoop K, Bensing S, Oksnes M, Esposito D, Bergthorsdottir R, Drake W, Wahlberg J, Reisch N, Hahner S, Pearce S, Trainer P, Etzrodt-Walter G, Thalmann SP, Saevik AB, Husebye E, Isidori AM, Falhammar H, Meyer G, Corsello SM, Pivonello R, Murray R, Bancos I, Quinkler M, Beuschlein F (2020)
Current Management and Outcome of Pregnancies in Women With Adrenal Insufficiency: Experience from a Multicenter Survey.
The Journal of Clinical Endocrinology & Metabolism 2020 Aug 1; 105(8): e2853-e2863
Zur Publikation

Burger-Stritt S, Eff A, Quinkler M, Kienitz T, Stamm B, Willenberg HS, Meyer G, Klein J, Reisch N, Droste M, Hahner S (2020)
Standardised patient education in adrenal insufficiency: a prospective multi-centre evaluation.
European Journal of Endocrinology 2020 Aug; 183(2): 119-127
Zur Publikation

Constantinescu G, Langton K, Conrad C, Amar L, Assie G, Gimenez-Roqueplo AP, Blanchard A, Larsen CK, Mulatero P, Williams TA, Prejbisz A, Fassnacht M, Bornstein S, Ceccato F, Fliedner S, Dennedy M, Peitzsch M, Sinnott R, Januszewicz A, Beuschlein F, Reincke M, Zennaro MC, Eisenhofer G, Deinum J (2020)
Glucocorticoid Excess in Patients with Pheochromocytoma Compared with Paraganglioma and Other Forms of Hypertension.
The Journal of Clinical Endocrinology & Metabolism 2020 Jul 1; 105(9): e3374–e3383
Zur Publikation

Deutschbein T, Jaursch-Hancke C, Fassnacht M (2020)
[Non-functioning pituitary tumors - short presentation of the first German guideline].
Deutsche Medizinische Wochenschrift 2020 Oct; 145(20): 1444-1449
Zur Publikation

Eisenhofer G, Deutschbein T, Constantinescu G, Langton K, Pamporaki C, Calsina B, Monteagudo M, Peitzsch M, Fliedner S, Timmers H, Bechmann N, Fankhauser M, Nolting S, Beuschlein F, Stell A, Fassnacht M, Prejbisz A, Lenders JWM, Robledo M (2020)
Plasma metanephrines and prospective prediction of tumor location, size and mutation type in patients with pheochromocytoma and paraganglioma.
Clinical Chemistry and Laboratory Medicine 2020 Oct 1; 59(2): 353-363
Zur Publikation

Fuss CT, Burger-Stritt S, Horn S, Koschker AC, Frey K, Meyer A, Hahner S (2020)
Continuous rhPTH (1-34) treatment in chronic hypoparathyroidism.
Endocrinology, Diabetes & Metabolism Case Reports 2020 May; 2020(1): EDM20-0009

Zur Publikation

Jiang J, Zhang J, Pang Y, Bechmann N, Li M, Monteagudo M, Calsina B, Gimenez-Roqueplo AP, Nolting S, Beuschlein F, Fassnacht M, Deutschbein T, Timmers H, Akerstrom T, Crona J, Quinkler M, Fliedner SMJ, Liu Y, Guo J, Li X, Guo W, Hou Y, Wang C, Zhang L, Xiao Q, Liu L, Gao X, Burnichon N, Robledo M, Eisenhofer G (2020)
Sino-European Differences in the Genetic Landscape and Clinical Presentation of Pheochromocytoma and Paraganglioma.
The Journal of Clinical Endocrinology & Metabolism 2020 Oct; 105(10): 3295–3307
Zur Publikation

Mende KC, Kellner T, Petersenn S, Honegger J, Evangelista-Zamora R, Droste M, Stalla G, Deutschbein T, Wang Y, Moskopp D, Knappe U, Schilbach K, Flitsch J (2020)
Clinical Situation, Therapy, and Follow-Up of Adult Craniopharyngioma.
The Journal of Clinical Endocrinology & Metabolism 2020 Jan; 105(1): 252–265
Zur Publikation.

Muller LM, Kienitz T, Deutschbein T, Riester A, Hahner S, Burger-Stritt S, Berr CM, Osswald A, Braun L, Rubinstein G, Reincke M, Quinkler M (2020)
Glucocorticoid Receptor Polymorphisms Influence Muscle Strength in Cushing's Syndrome.
The Journal of Clinical Endocrinology & Metabolism 2020 Jan 1; 105(1): 305–313
Zur Publikation

Vogel F, Braun LT, Rubinstein G, Zopp S, Kunzel H, Strasding F, Albani A, Riester A, Schmidmaier R, Bidlingmaier M, Quinkler M, Deutschbein T, Beuschlein F, Reincke M (2020)
Persisting Muscle Dysfunction in Cushing's Syndrome Despite Biochemical Remission.
The Jorunal of Clinical Endocrinology & Metabolism 2020 Dec 1; 105(12): e4490–e4498
Zur Publikation

Weigand I, Schreiner J, Rohrig F, Sun N, Landwehr LS, Urlaub H, Kendl S, Kiseljak-Vassiliades K, Wierman ME, Angeli JPF, Walch A, Sbiera S, Fassnacht M, Kroiss M (2020)
Active steroid hormone synthesis renders adrenocortical cells highly susceptible to type II ferroptosis induction.
Cell Death & Disease 2020 Mar 17; 11(3): 192

Zur Publikation

2019

Barthel A, Benker G, Berens K, Diederich S, Manfras B, Gruber M, Kanczkowski W, Kline G, Kamvissi-Lorenz V, Hahner S, Beuschlein F, Brennand A, Boehm BO, Torpy DJ, Bornstein SR (2019)
An Update on Addison's Disease
Experimental and Clinical Endocrinology and Diabetes 2019; 127(2-03): 165-175
Zur Publikation 

Burger-Stritt S, Bachmann L, Kurlbaum M, Hahner S (2019)
Emergency treatment of adrenal crisis with prednisone suppositories: a bioequivalence study in female patients with Addison's disease.
Endocrine Connections 2019 Apr 1; 8(4): 425-434
Zur Publikation

Manetti L, Deutschbein T, Schopohl J, Yuen KCJ, Roughton M, Kriemler-Krahn U, Tauchmanova L, Maamari R, Giordano C (2019)
Long-term safety and efficacy of subcutaneous pasireotide in patients with Cushing's disease: interim results from a long-term real-world evidence study.
Pituitary 2019 Aug 22; 22(5): 542-551
Zur Publikation

Christa M, Weng AM, Geier B, Wörmann C, Scheffler A, Lehmann L, Oberberger J, Kraus BJ, Hahner S, Störk S, Klink T, Bauer WR, Hammer F, Köstler H (2019)
Increased myocardial sodium signal intensity in Conn's syndrome detected by 23Na magnetic resonance imaging.
European Heart Journal Cardiovascular Imaging 2019 Mar 1; 20(3): 263-270
Zur Publikation

Mangelis A, Jühlen R, Dieterich P, Peitzsch M, Lenders JWM, Hahner S, Schirbel A, Eisenhofer GJS (2019)
A steady state system for in vitro evaluation of steroidogenic pathway dynamics: Application for CYP11B1, CYP11B2 and CYP17 inhibitors.
The Journal of Steroid Biochemistry and Molecular Biology 2019 Apr; 188: 38-47
Zur Publikation

Osswald A, Quinkler M, Di Dalmazi G, Deutschbein T, Rubinstein G, Ritzel K, Zopp S, Bertherat J, Beuschlein B, Reincke M (2019)
Long-Term Outcome of Primary Bilateral Macronodular Adrenocortical Hyperplasia After Unilateral Adrenalectomy.
The Journal of Clinical Endocrinology & Metabolism 2019 Jul 1; 104(7): 2985-2993
Zur Publikation

Popp KH, Kosilek RP, Frohner R, Stalla GK, Athanasoulia-Kaspar AP, Berr CM, Zopp S,  Reincke M, Witt M, Würtz RP, Deutschbein T, Quinkler M, Schneider HJ (2019)
Computer Vision Technology in the Differential Diagnosis of Cushing's Syndrome.
Experimental and Clinical Endocrinology and Diabetes 2019 Oct; 127(10): 685-690
Zur Publikation

Refardt J, Sailer CO, Chifu I, Winzeler B, Schnyder I, Fassnacht M, Fenske WK, Christ-Crain M (2019)
The challenges of sodium measurements - indirect versus direct ion selective method.
European Journal of Endocrinology 2019 Jun 1; 181(2): 193-199
Zur Publikation

Sbiera S, Perez-Rivas LG, Taranets L, Weigand I, Flitsch J, Graf E, Monoranu CM, Saeger W, Hagel C, Honegger J, Assie G, Hermus AR, Stalla GK, Herterich S, Ronchi CL, Deutschbein T, Reincke M, Strom TM, Popov N, Theodoropoulou M, Fassnacht M (2019)
Driver mutations in USP8 wild-type Cushing's disease.
Neuro-Oncology 2019 Oct; 21(10): 1273-1283
Zur Publikation

Sbiera S, Kunz M, Weigand I, Deutschbein T, Dandekar T, Fassnacht M (2019)
The New Genetic Landscape of Cushing's Disease: Deubiquitinases in the Spotlight.
Cancers (Basel) 2019 Nov 8; 11(11): 1761
Zur Publikation

Schweitzer S, Kunz M, Kurlbaum M, Vey J, Kendl S, Deutschbein T, Hahner S, Fassnacht M, Dandekar T, Kroiss M (2019)
Plasma steroid metabolome profiling for the diagnosis of adrenocortical carcinoma.
European Journal of Endocrinology 2019 Feb 1; 180(2): 117-125
Zur Publikation 

Weigand I, Knobloch L, Flitsch J, Saeger W, Monoranu CM, Höfner K, Herterich S, Rotermund R, Ronchi CL, Buchfelder M, Glatzel M, Hagel C, Fassnacht M, Deutschbein T, Sbiera S (2019)
Impact of USP8 Gene Mutations on Protein Deregulation in Cushing Disease.
The Journal of Clinical Endocrinology & Metabolism 2019; 104(7): 2535-2546
Zur Publikation

Winzeler B, Cesana-Nigro N, Refardt J, Vogt DR, Imber C, Morin B, Popovic M, Steinmetz M, Sailer CO, Szinnai G, Chifu I, Fassnacht M, Christ-Crain M (2019)
Arginine-stimulated copeptin measurements – a new test for diabetes insipidus.
The Lancet 2019 Aug 17; 394(10198): 587-595
Zur Publikation

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